An interventricular membranous septal aneurysm obstructing the right ventricle outflow tract in a five-year-old boy: a c
- PDF / 665,237 Bytes
- 4 Pages / 595.276 x 790.866 pts Page_size
- 65 Downloads / 161 Views
(2020) 15:297
CASE REPORT
Open Access
An interventricular membranous septal aneurysm obstructing the right ventricle outflow tract in a five-year-old boy: a case report Lubna Bakr* , Mohammad Al-Jadaan and Mohammad Younes
Abstract Background: While the aneurysms of the membranous septum (AVS) are rare, the possibility that they lead to obstruction is even rarer. To the best of our knowledge, 11 similar cases have been reported since 1982. Case presentation: Initially, the five-year-old boy was evaluated for dyspnoea that had been present since birth. He did not receive any medical treatment until the previous year. At the age of four, the transthoracic echocardiography showed a large aneurysm extending to the right ventricular outflow tract (RVOT) and causing RVOT stenosis. Complete surgical resection of the aneurysmal tissue was performed, and the boy was discharged home in satisfactory condition. Conclusions: As the occurrence of RVOT obstruction by a membranous ventricular septal aneurysm is very rare, we are reporting the second case in which an aneurysm of the membranous septum dynamically obstructed the RVOT in a child. We are also reviewing all the previously reported similar cases in the literature. Further studies are needed to obtain a more comprehensive understanding of aneurysms of the membranous septum (AVS). Keywords: Aneurysm of the membranous septum, Right ventricular outflow tract, Ventricular septal defect, Cardiac surgery, Case report
Background An aneurysm of the membranous portion of the ventricular septum is a rare congenital anomaly, occurring alone or in combination with other cardiac lesions, and is usually of no clinical significance [1]. Ventricular septal defect (VSD) is the most common congenital heart malformation (30–40%), as an isolated finding [2]. Although it can be associated with other congenital defects, only few cases were reported to be associated with an interventricular membranous septal aneurysm leading to obstruction of the right ventricle outflow tract (RVOT). To the best of our knowledge, this is the second reported case in which an * Correspondence: [email protected] Department of Cardiac Surgery, Faculty of Medicine, Damascus University, Damascus, Syria
aneurysm of the membranous septum dynamically obstructed the RVOT in a child.
Case presentation Initially, the boy was evaluated for dyspnoea that had been present since birth. He was diagnosed with a ventricular septum defect (VSD). He was followed by a pediatric cardiologist. He did not receive any medical treatment until the previous year. At the age of four, the transthoracic echocardiography showed a large aneurysm extending to the right ventricular outflow tract and causing RVOT stenosis (peak gradient = 83 mmHg). The patient was admitted to the cardiac surgery department by the age of five. His mother reported a recurrent upper respiratory tract infection (RTI) throughout his life.
© The Author(s). 2020 Open Access This article is licensed under a Creative Commons Attribution 4.0 International Licens
Data Loading...
