Self-healing juvenile cutaneous mucinosis, a sclerodermoid disorder simulating juvenile dermatomyositis: a case-based re
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Rheumatology International https://doi.org/10.1007/s00296-020-04578-5
INTERNATIONAL
CASE BASED REVIEW
Self‑healing juvenile cutaneous mucinosis, a sclerodermoid disorder simulating juvenile dermatomyositis: a case‑based review Anuradha Bishnoi1 · Ankur Kumar Jindal2 · Gummadi Anjani2 · Pratap Kumar Patra2 · Debajyoti Chatterjee3 · Keshavamurthy Vinay1 · Amrinder J. Kanwar4 · Sunil Dogra1 · Surjit Singh2 Received: 2 January 2020 / Accepted: 7 April 2020 © Springer-Verlag GmbH Germany, part of Springer Nature 2020
Abstract Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare childhood disease with characteristic cutaneous and rheumatic manifestations. Cutaneous manifestations include a combination of nodules affecting peri-articular (especially interphalangeal joints) and head and neck areas; and linearly arranged ivory white papules over an erythematous indurated skin. Despite a benign course, an abrupt onset of symptoms with extensive cutaneous involvement often leads to parental anxiety, overenthusiastic evaluation and sometimes aggressive treatment. A peculiar cutaneous distribution in SHJCM including nodular lesions and periorbital edema, arthritis and arthralgia in a few cases, may simulate juvenile dermatomyositis. It is, therefore, important for dermatologists and pediatricians to be aware of this entity. In this report, we describe two cases of SHJCM and briefly review similarly reported cases in children. Keywords Self-healing juvenile cutaneous mucinosis · Juvenile dermatomyositis · Scleromyxedema
Introduction
Anuradha Bishnoi, Ankur Kumar Jindal, and Gummadi Anjani contributed equally to the manuscript as first authors. Electronic supplementary material The online version of this article (https://doi.org/10.1007/s00296-020-04578-5) contains supplementary material, which is available to authorized users.
Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare childhood disease with characteristic cutaneous and rheumatic manifestations. Cutaneous manifestations include a combination of nodules affecting periarticular (especially interphalangeal joints) and head and neck areas; and linearly arranged ivory white papules over an erythematous
* Keshavamurthy Vinay [email protected]
Surjit Singh [email protected]
Anuradha Bishnoi [email protected]
1
Department of Dermatology, Venereology and Leprology, Postgraduate Institute of Medical Education and Research, Chandigarh 160012, India
2
Department of Pediatric Clinical Immunology and Rheumatology, Allergy Immunology Unit, Postgraduate Institute of Medical Education and Research, Advanced Pediatric Center, Chandigarh 160012, India
3
Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh 160012, India
4
Dr AJ Kanwar Skin Clinic, Greater Kailash, New Delhi 110048, India
Ankur Kumar Jindal [email protected] Gummadi Anjani [email protected] Pratap Kumar Patra [email protected] Debajyoti Chatterjee [email protected]
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