Epithelioid hemangioendothelioma of the right atrium invaded the superior vena cava: case report and review of literatur
- PDF / 5,205,864 Bytes
- 6 Pages / 595.276 x 790.866 pts Page_size
- 86 Downloads / 189 Views
CASE-IN-POINT
Epithelioid hemangioendothelioma of the right atrium invaded the superior vena cava: case report and review of literature Wenpeng Huang1 · Liming Li1 · Jianbo Gao1 · Jian‑Bo Gao1 Received: 31 July 2020 / Accepted: 5 August 2020 © The Author(s) 2020
Abstract Epithelioid hemangioendothelioma (EHE) is a rare hemangioma that can occur anywhere in the body. It occurs most commonly in the liver and lungs, rarely from the heart, and the etiology or risk factors are unclear. So far, timely detection and radical resection is a more acceptable treatment. Reviewing the literature, few cases of cardiac EHE have been reported. We present a rare case of EHE of the right atrium invaded the superior vena cava. Keywords Heart neoplasms · Epithelioid hemangioendothelioma · Tomography, X-ray computed · Magnetic resonance imaging Abbreviations EHE Epithelioid hemangioendothelioma CT Computed tomography MRI Magnetic resonance imaging FLI-1 Friend leukemia integration 1
Introduction Epithelioid hemangioendothelioma (EHE) is a rare lowgrade malignant angiogenic tumor with local invasiveness and metastatic potential. EHE is a rare low-grade malignant angiogenic tumor with local invasiveness and metastatic potential. Clinically, EHE can occur simultaneously or sequentially in many parts, such as lung, liver, bone, soft tissue and other organs, and there is no obvious specificity in clinical symptoms. There are few case reports of EHE in the literature. We report a unique case of EHE of the right atrium invaded the superior vena cava and review of the literature.
* Jian‑Bo Gao [email protected] 1
Department of Radiology, The First Affiliated Hospital of Zhengzhou University, No.1 Eastern Jianshe Road, Zhengzhou 450052, China
Case report A 54-year-old man had intermittent chest tightness for 49 years. There was no obvious inducement of facial and eyelid edema 2 months ago, and it was aggravated when he got up in the morning. However, physical examination found that the patient did not have dyspnea, hemoptysis, cyanosis, limb edema, sensory abnormalities and other symptoms. There is no previous history of surgery or other diseases. Laboratory examination showed that hemoglobin 115.0 g/L, erythrocyte 3.63 × 1012, 24-h urine protein and tumor markers were not abnormal. After admission, the cardiac function of the patient was examined. First, echocardiography showed that the right atrium near the entrance of the superior vena cava could be hypoechoically attached to the heart wall, with an area of about 22 mm × 16 mm (Fig. 1a). The fluid dark area was detected in the pericardium. Ultrasound doctors considered the formation of emboli extending from the right atrium to the entrance of the inferior vena cava. Subsequently, the patient underwent cardiac magnetic resonance imaging, showing a massive low-signal shadow in the right atrium on the trufi sequence (Fig. 1b). The right atrium was small and the right ventricle was large, so delayed contrast-enhanced scan was performed 2 h later. After intravenous injection
Data Loading...
