Quality of Life Evaluation Following Limb Lengthening Surgery in Patients with Achondroplasia
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ORIGINAL ARTICLE
Quality of Life Evaluation Following Limb Lengthening Surgery in Patients with Achondroplasia Sefa Giray Batıbay1 · Halil İbrahim Balcı2 · Serkan Bayram2 · Mehmet Chodza2 · Şeyda Göksoy3 · Önder Murat Hürmeydan4 · Aslı Derya Kardelen5 · Cengiz Şen2 · Mehmet Kocaoğlu6 Received: 29 March 2020 / Accepted: 22 April 2020 / Published online: 4 May 2020 © Indian Orthopaedics Association 2020
Abstract Background The primary objective of this study was to evaluate the quality of life following limb lengthening surgery in patients with achondroplasia. The complications and different lengthening techniques have and effects on mid-term results were also investigated. Methods We performed a retrospective, multicenter study by evaluating the records of patients with achondroplasia operated in our clinic between 1999 and 2014 for limb lengthening with a minimum follow-up of 3 years. Forty nine patients were underwent bilateral lower limb lengthening surgery and 21 of 49 patients underwent bilateral humerus lengthening surgery. Patients were evaluated by the Pediatric Quality of Life Inventory (PedsQL) 4.0 Generic Core Scales to assess the health-related quality of life (HRQOL) of children. Twenty patients with achondroplasia who had no lengthening surgery history were also evaluated with the PedsQL score as the control group. Results The average age at the time of first surgery was 6.17 years. The average follow-up period was 100.2 months. The average age at the time of study 14.70 ± 2.44 (11–18) years. There were significant differences between the patients with humeral lengthening and patients who did not undergo humeral lengthening in all scores. Transient complications had minimal effects on scores. Although all scores in the operated group were higher than non-operated patients with achondroplasia, there were no significant differences. Conclusion Quality of life was significantly improved as a result of humerus lengthening surgery of patients with achondroplasia, despite minor complications compared with Lower limb lengthening surgery. Level of Evidence Level III, case control study. Keywords Congenital short extremity · Lengthening rhythm · Congenital femoral deficiency · Congenital tibia pseudarthrosis · Quality of callus * Serkan Bayram [email protected]
Introduction
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Patients with achondroplasia have physical and psychological limitations owing to the disproportionate stature of the body and difficulty in making routine activities of daily life such as perianal-perineal hygiene and decreased walking distance [1, 2]. Limb lengthening surgery is usually required for both the upper and lower limbs of these patients [1–3]. According to the literature, 85% of these patients were satisfied with their improved physical and psychological status as a result of the lengthening surgery [3]. There are many tests for assessing the quality of life outcomes for children and adolescents. The Pediatric Quality of Life Inventory (PedsQL) is considered one of the most promising health-related quality
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